Amish, Mennonite, and Hutterite
Genetic Disorder Database

Cardiomyopathy, dilated, 1A

Disorder
OMIM #: #115200  (Click to access OMIM database)
Disorder: Cardiomyopathy, dilated, 1A 
Also known as: CMD1A
CARDIOMYOPATHY, DILATED, WITH CONDUCTION DEFECT 1
CDCD1, CARDIOMYOPATHY, IDIOPATHIC DILATED, CARDIOMYOPATHY, FAMILIAL IDIOPATHIC, CARDIOMYOPATHY, CONGESTIVE 
Clinical
Phenotype: dilated cardiomyopathy, atrial fibrillation, arrhythmia, heart failure, sudden death 
Seen In: Amish
Old Order Mennonite
Old Colony Mennonite
Unknown/Other Mennonite
Hutterite
Remarks: Autosomal dominant 
Mutations
1   Amish  
Gene: LMNA
Base Change: C>T, at nucleotide 568
Amino Acid Change: arg 190 --> trp
2   Amish  
Gene: LMNA
Base Change: C>T, at nucleotide 232
Amino Acid Change: arg 78 --> trp
Last updated: 2023-02-01 

References
Lynch MT, Maloney KA, Pollin TI, Streeten EA, Xu H; Regeneron Genetics Center, Shuldiner AR, Van Hout CV, Gonzaga-Jauregui C, Mitchell BD. (2021) The burden of pathogenic variants in clinically actionable genes in a founder population. Am J Med Genet A Aug 31. doi: 10.1002/ajmg.a.62472.
PubMed ID: 34467620 
Strauss KA, Puffenberger EG. (2009) Genetics, medicine, and the Plain people. Annu Rev Genomics Hum Genet 10:513-36.
PubMed ID: 19630565 

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