Amish, Mennonite, and Hutterite
Genetic Disorder Database

Fraser syndrome

Disorder
OMIM #: #219000  (Click to access OMIM database)
Disorder: Fraser syndrome 
Also known as: Cryptophthalmos with other malformations 
Clinical
Phenotype: cryptophthalmos, blindness, hypoplasia of nares, broad nasal bridge, low nasal bridge, cleft palate, cleft lip, malformed auricles, laryngeal stenosis, laryngeal atresia, cutaneous syndactyly, genitourinary anomalies, renal agenesis, developmental delay 
Seen In: Amish
Old Order Mennonite
Old Colony Mennonite
Unknown/Other Mennonite
Hutterite
Remarks:

Testing is available at LHSC.

Autosomal recessive 

Mutations
1   Amish  
Gene: FRAS1
Base Change: c.748_758del11
Amino Acid Change: Frame shift
Last updated: 2022-11-04 

References
Siu VM, Lahiry P, Hegele RA, Rupar CA. (2015) MG-137 Autosomal recessive disorders are common in the old order amish population of southwestern ontario. J Med Genet 52(1).  

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