Amish, Mennonite, and Hutterite
Genetic Disorder Database

Spastic paraplegia 56

Disorder
OMIM #: #615030  (Click to access OMIM database)
Disorder: Spastic paraplegia 56 
Also known as: SPG56 
Clinical
Phenotype: early-onset progressive lower-limb spasticity, upper limbs spasticity, subclinical axonal neuropathy in some patients 
Seen In: Amish
Old Order Mennonite
Old Colony Mennonite
Unknown/Other Mennonite
Hutterite
Remarks: Autosomal recessive 
Mutations
1   Old Order Mennonite  
Gene: CYP2U1
Base Change: c.1206_1207delAG
Amino Acid Change:
Last updated: 2022-11-13 

References
Personal communication; seen at CSC.  

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