Amish, Mennonite, and Hutterite
Genetic Disorder Database

Albinism, oculocutaneous, type II

Disorder
OMIM #: #203200  (Click to access OMIM database)
Disorder: Albinism, oculocutaneous, type II 
Also known as: OCULOCUTANEOUS ALBINISM, TYPE II
OCULOCUTANEOUS ALBINISM, TYROSINASE-POSITIVE
ALBINISM II  
Clinical
Phenotype: completely hypopigmented skin at birth with little change upon aging, decreased visual acuity, nystagmus, ocular albinism, unusual patterning or coloration of iris, foveal hypoplasia, strabismus, hyperopia, myopia, astigmatism, visible choroidal vessels 
Seen In: Amish
Old Order Mennonite
Old Colony Mennonite
Unknown/Other Mennonite
Hutterite
Remarks:  
Mutations
1   Old Order Mennonite  
Gene: OCA2
Base Change: A>G, at nucleotide 823
Amino Acid Change: thr 275 --> ala
2   Old Order Mennonite  
Gene: OCA2
Base Change: G>T, at nucleotide 2433
Amino Acid Change: arg 811 --> ser
Last updated: 2022-11-01 

References
Strauss KA, Gonzaga-Jauregui C, Brigatti KW, Williams KB, King AK, Van Hout C, Robinson DL, Young M, Praveen K, Heaps AD, Kuebler M, Baras A, Reid JG, Overton JD, Dewey FE, Jinks RN, Finnegan I, Mellis SJ, Shuldiner AR, Puffenberger EG. (2018) Genomic diagnostics within a medically underserved population: efficacy and implications. Genet Med Jan;20(1):31-41.
PubMed ID: 28726809 

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